About 10% of children with rheumatic fever due to a group A streptococcal tonsillitis develop an inflammatory brain condition with St. Vitus Dance (also called “Sydenham’s chorea”).
This is due to a cross reactivitiy between streptococcal antigens and brain tissue, which have a resemblance, and this leads to an inflammatory reaction in the brain and an associated neurological condition.
The patient develops rapid involuntary movements that disappear during the sleep. Facial grimacing is common. In mild cases there might only be a certain clumsiness or having problems with dressing or eating. The condition lasts 3 to 6 months. It occurs more so in girls than boys and is often associated with rheumatic fever. The diagnosis of St. Vitus dance is mostly clinical and done by a neurologist. Here is a You Tube video of St. Vitus Dance.
EEGs show only non specific changes. The condition is self limiting and is only a transitory phenomenon and part of rheumatic fever. Occasionally the specialist may treat the condition with small amounts of benzodiazepines or antipsychotics (Ref. 7).
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